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KMID : 0191119910060040362
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Journal of Korean Medical Science
1991 Volume.6 No. 4 p.362 ~ p.366
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Congenital arteriovenous malformation associated with progressive hydrocephalus in a newborn
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Park SH
Chi JG/Cho BK
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Abstract
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Intracranial arteriovenous malformation is rarely presented in newborns or infants. We describe
an unusual case of congenital arteriovenous malformation of the brain with multiple sequestered
grape-like venous sacs presented with congenital hydrocephalus. This 4-month-old girl born with
a large head, presented with progressive hydrocephalus over a period of 4 months. The brain CT
showed multiloculated cysts with a high-density mural nodule and thin cerebral mantle. The right
lateral ventricle was collapsed by the cystic lesion, and the contralateral ventricle was markedly
dilated, which was thought to be due to aqueductal obstruction by the conglomerated nidus of the
arteriovenous malformation. Surgical removal of both hemispheric masses, including the overlying
thin mantle. The lesion was pathologically confirmed as the arteriovenous malformation which was
composed of markedly dilated veins and multiple sequestered aneurysmal sacs. The overlying cerebral
tissue was dysplastic and partly infarcted. This case shows that intracerebral arteriovenous
malformation is indeed a congenital anomaly and suggests that intrauterine vascular compromise
can result in focal or wide maldevelopment of the brain.
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